{"id":96618,"date":"2023-06-11T10:21:02","date_gmt":"2023-06-11T10:21:02","guid":{"rendered":"https:\/\/haberulus.net\/?p=96618"},"modified":"2023-06-11T10:21:02","modified_gmt":"2023-06-11T10:21:02","slug":"kacis-sendromu-nedir-belirtileri-neler","status":"publish","type":"post","link":"https:\/\/haberulus.net\/?p=96618","title":{"rendered":"Ka\u00e7\u0131\u015f sendromu nedir, belirtileri neler?"},"content":{"rendered":"<p>D\u00fcnya \u00fczerinde \u00e7ok nadir g\u00f6r\u00fclen bir hastal\u0131k olan ka\u00e7\u0131\u015f sendromu ilk kez 1960 y\u0131l\u0131nda Dr. Clarkson ve arkada\u015flar\u0131 taraf\u0131ndan ke\u015ffedilmi\u015ftir. Sistemik k\u0131lcal ka\u00e7ak sendromu olarakta bilinen ka\u00e7\u0131\u015f sendromu nedir? Ka\u00e7\u0131\u015f sendromu nedenleri, belirtileri ve tedavisi hakk\u0131nda merak edilen t\u00fcm detaylar\u0131 haberimizde bulabilirsiniz\u2026<\/p>\n<p><strong>KA\u00c7I\u015e SENDROMU NED\u0130R?<\/strong><\/p>\n<p>Ka\u00e7ak sendromu bir ba\u015fka isimle sistemik k\u0131lcal ka\u00e7ak sendromu (SCLS), kan damarlar\u0131ndan kom\u015fu v\u00fccut kavitelerine (bo\u015fluk) ve kaslar\u0131na tekrarlayan b\u00fcy\u00fck miktarda plazma s\u0131z\u0131nt\u0131s\u0131 ile karakterize nadir g\u00f6r\u00fclen bir hastal\u0131kt\u0131r. Bu, kan bas\u0131nc\u0131nda, tedavi edilmedi\u011finde organ yetmezli\u011fine ve \u00f6l\u00fcme neden olabilecek keskin bir d\u00fc\u015f\u00fc\u015fe neden olur.<\/p>\n<p>Clarkson hastal\u0131\u011f\u0131 olarak da adland\u0131r\u0131lan bu durum, yayg\u0131n enfeksiyonlara (septik \u015fok) veya ciddi alerjik reaksiyonlara (anafilaktik \u015fok) ciddi reaksiyonlar ile kar\u0131\u015ft\u0131r\u0131labilir. Ataklar\u0131n s\u0131kl\u0131\u011f\u0131, \u00f6m\u00fcr boyu bir y\u0131ldan birka\u00e7 y\u0131la kadar de\u011fi\u015febilir. Baz\u0131lar\u0131 ise ya\u015famlar\u0131 boyunca sadece bir atak ge\u00e7irirler.<\/p>\n<p><img decoding=\"async\" src=\"https:\/\/i01.sozcucdn.com\/wp-content\/uploads\/2023\/06\/11\/karin-agrisi-shutterstock.jpg\" alt=\"\" title=\"\"><\/p>\n<p><strong>KA\u00c7I\u015e SENDROMU BEL\u0130RT\u0130LER\u0130<\/strong><\/p>\n<p>\u2013 Sinirlilik<br \/>\u2013 Yorgunluk<br \/>\u2013 Kar\u0131n a\u011fr\u0131s\u0131<br \/>\u2013 Mide bulant\u0131s\u0131<br \/>\u2013 Kas a\u011fr\u0131lar\u0131<br \/>\u2013 A\u015f\u0131r\u0131 susama<br \/>\u2013 V\u00fccut a\u011f\u0131rl\u0131\u011f\u0131nda ani art\u0131\u015f<\/p>\n<p><strong>KA\u00c7IS SENDROMU NEDENLER\u0130<\/strong><\/p>\n<p>Bir\u00e7ok durumda neden bilinmemektedir (idiyopatik SCLS). SCLS\u2019li baz\u0131 ki\u015filer, ataklardan \u00f6nce bir enfeksiyon (vir\u00fcs gibi) ge\u00e7irdi\u011fini bildirmi\u015ftir. Baz\u0131 ka\u00e7\u0131\u015f sendromu vakalar\u0131, kalbin, b\u00f6bre\u011fin veya karaci\u011ferin \u00e7e\u015fitli durumlar\u0131yla ili\u015fkilidir. Bir epizod s\u0131ras\u0131nda tedavi, hava yolu ve solunumun stabilize edilmesini ve s\u0131v\u0131lar\u0131n, ila\u00e7lar\u0131n veya kan \u00fcr\u00fcnlerinin inf\u00fczyonunu i\u00e7erebilir. Gelecekteki ataklar\u0131 \u00f6nlemek i\u00e7in periyodik inf\u00fczyonlar veya baz\u0131 ila\u00e7lar kullan\u0131labilir.<\/p>\n<p><strong>KA\u00c7I\u015e SENDROMU TEDAV\u0130S\u0130<\/strong><\/p>\n<p>\u015eu anda sistemik k\u0131lcal ka\u00e7ak sendromu (SCLS) i\u00e7in bir tedavi yoktur. Bir atak s\u0131ras\u0131nda SCLS tedavisi \u00e7o\u011funlukla destekleyici olup, semptomlar\u0131 stabilize etmeyi ve ciddi komplikasyonlar\u0131 \u00f6nlemeyi ama\u00e7lamaktad\u0131r. Bu, hava yolu ve solunumun stabilize edilmesini, belirli ila\u00e7lar\u0131n al\u0131nmas\u0131n\u0131 ve \/ veya intraven\u00f6z (IV) s\u0131v\u0131, ila\u00e7 veya kan \u00fcr\u00fcnleri inf\u00fczyonunu i\u00e7erebilir. Baz\u0131lar\u0131 IV s\u0131v\u0131lar\u0131n\u0131n \u015fi\u015fmeyi (\u00f6dem) k\u00f6t\u00fcle\u015ftirebilece\u011fi veya ba\u015fka komplikasyonlar\u0131n riskini art\u0131rabilece\u011fi i\u00e7in tavsiye edilmedi\u011fini \u00f6ne s\u00fcrmektedir. Bir ki\u015fi iyile\u015fmeye ba\u015flad\u0131\u011f\u0131nda, di\u00fcretikler (idrar at\u0131m\u0131n\u0131 kolayla\u015ft\u0131ran ila\u00e7lar) hemen her zaman gereklidir.<\/p>\n<p>Periyodik inf\u00fczyonlar veya belirli ila\u00e7lar\u0131n kullan\u0131m\u0131, gelecekteki ataklar\u0131 \u00f6nlemeye \u00e7al\u0131\u015fmak i\u00e7in kullan\u0131l\u0131r (profilaktik tedavi). Ayl\u0131k intraven\u00f6z imm\u00fcn globulin inf\u00fczyonlar\u0131 (IVIG) \u00f6nerilmi\u015ftir. 2017 y\u0131l\u0131nda yay\u0131nlanan bir \u00e7al\u0131\u015fmada, ka\u00e7\u0131\u015f sendromu olan ki\u015filerde \u0130V\u0130G ile \u00f6nleyici tedavinin sa\u011fkal\u0131mla ili\u015fkili en g\u00fc\u00e7l\u00fc fakt\u00f6r oldu\u011fu bulunmu\u015ftur. \u0130V\u0130G ile d\u00fczelmeyen ya da tedaviye tahamm\u00fcl edemeyenler teofilin ve terbutalin ile ba\u015far\u0131l\u0131 olabilirler.<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Ka\u00e7ak sendromu bir ba\u015fka isimle sistemik k\u0131lcal ka\u00e7ak sendromu (SCLS), damarlar\u0131ndan kom\u015fu v\u00fccut kavitelerine (bo\u015fluk) ve kaslar\u0131na tekrarlayan b\u00fcy\u00fck miktarda plazma s\u0131z\u0131nt\u0131s\u0131 ile karakterize nadir g\u00f6r\u00fclen bir hastal\u0131kt\u0131r. Ka\u00e7\u0131\u015f sendromu belirtileri aras\u0131nda v\u00fccut a\u011f\u0131rl\u0131\u011f\u0131nda ani art\u0131\u015f, a\u015f\u0131r\u0131 susama ve sinirlilik semptomlar yer al\u0131yor.<\/p>\n","protected":false},"author":1,"featured_media":96619,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[30],"tags":[12307,955,10829,12306,376],"class_list":["post-96618","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-saglik","tag-atak","tag-bazi","tag-ilaclar","tag-kacis-sendromu","tag-tedavi"],"_links":{"self":[{"href":"https:\/\/haberulus.net\/index.php?rest_route=\/wp\/v2\/posts\/96618","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/haberulus.net\/index.php?rest_route=\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/haberulus.net\/index.php?rest_route=\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/haberulus.net\/index.php?rest_route=\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/haberulus.net\/index.php?rest_route=%2Fwp%2Fv2%2Fcomments&post=96618"}],"version-history":[{"count":1,"href":"https:\/\/haberulus.net\/index.php?rest_route=\/wp\/v2\/posts\/96618\/revisions"}],"predecessor-version":[{"id":96620,"href":"https:\/\/haberulus.net\/index.php?rest_route=\/wp\/v2\/posts\/96618\/revisions\/96620"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/haberulus.net\/index.php?rest_route=\/wp\/v2\/media\/96619"}],"wp:attachment":[{"href":"https:\/\/haberulus.net\/index.php?rest_route=%2Fwp%2Fv2%2Fmedia&parent=96618"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/haberulus.net\/index.php?rest_route=%2Fwp%2Fv2%2Fcategories&post=96618"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/haberulus.net\/index.php?rest_route=%2Fwp%2Fv2%2Ftags&post=96618"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}